How strict is galactose restriction in adults with galactosaemia? International practice
Adam, Siddig Momin; Akroyd, R.; Bernabei, S.; Bollhalder, S.; Boocock, S.; Burlina, A.; Coote, T.; Corthouts, K.; Dalmau, Judith; Dawson, S.; Defourny, S.; Meyer, A.; Desloovere, A.; Devlin, Y.; Diels, M.; Dokoupil, K.; Donald, S.; Evans, S.; Fasan, I.; Ferguson, C.; Ford, S.; Forga, M.; Gallo, G.; Grünert, S.C.; Heddrich-Ellerbrok, M.; Heidenborg, C.; Jonkers, C.F.; Lefebure, K.; Luyten, K.; MacDonald, A.; Meyer, U.; Micciche, A.; Müller, E.; Portnoi, P.; Ripley, S.; Robert, C.M.; Robertson, L.V.; Rosenbaum-Fabian, S.; Sahm, K.; Schultz, Erica S; Singleton, K.; Sjöqvist, E.; Stoelen, L.; Terry, A.; Thompson, S.; Timmer, C.; Vande Kerckhove, K.; van den Ploeg, L.; Van Driessche, M.; van Rijn, M.; van Teeffelen-Heithoff, A.; Vitoria, I.; Voillot, C.; Wenz, J.; Westbrook, M.; Wildgoose, J.; Zweers, H.
(2015) Molecular Genetics and Metabolism, volume 115, issue 1, pp. 23 - 26
(Article)
Abstract
Dietary management of 418 adult patients with galactosaemia (from 39 centres/12 countries) was compared. All centres advised lactose restriction, 6 restricted galactose from galactosides. ±. fruits and vegetables and 12 offal. 38% (n. =. 15) relaxed diet by: 1) allowing traces of lactose in manufactured foods (n. =. 13) or
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2) giving fruits, vegetables and galactosides (n. =. 2). Only 15% (n. =. 6) calculated dietary galactose. 32% of patients were lost to dietetic follow-up. In adult galactosaemia, there is limited diet relaxation. © 2015 Elsevier Inc..
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Keywords: Galactosaemia, Galactose, Lactose, Galactose-1-phosphate, Diet, Monitoring, controlled study, diet restriction, diet therapy, dietary intake, dietetics, dietitian, disease severity, follow up, food processing, fruit, galactose restriction, galactosemia, health survey, human, major clinical study, multicenter study, priority journal, vegetable, clinical trial, comparative study, diet, food, questionnaire, Adult, Food, Fruit, Galactosemias, Humans, Surveys and Questionnaires, Vegetables
ISSN: 1096-7192
Publisher: Academic Press Inc.
Note: cited By 1
(Peer reviewed)